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Exhibit 21.1

SUBSIDARIES OF KINIKSA PHARMACEUTICALS INTERNATIONAL, PLC

The following subsidiaries are owned directly or indirectly by Kiniksa Pharmaceuticals International, plc:

Legal Name of
Subsidiary

 

Jurisdiction of
Organization

Kiniksa Pharmaceuticals Corp.

 

Delaware

Kiniksa Pharmaceuticals (France) SARL

 

France

Kiniksa Pharmaceuticals (Germany) GmbH

 

Germany

Kiniksa Pharmaceuticals, GmbH

 

Switzerland

Kiniksa Pharmaceuticals (UK), Ltd.

 

United Kingdom

Primatope Therapeutics, Inc.

 

Delaware